KUMJ | VOL. 10 | NO. 3 | ISSUE 39 | JUL-SEP, 2012
Eosinophilic Fascitis: A Rare Fibrosing Disorder
Paudyal BP, Gyawalee M, Sigdel K
Abstract: Eosinophilic fasciitis is a rare systemic disease characterized by inflammatory
thickening of the skin and underlying fascia, peripheral eosinophilia, elevated
inflammatory markers and typical biopsy findings. Internal organ involvement is
rare unlike in other fibrosing disorders. Though this is usually a benign disease, it
is often difficult to diagnose and the course may also be variable. Glucocorticoids
are the mainstay of therapy, but in many cases steroid sparing immunosuppressive
drugs are required particularly if the diseases has protracted course. The author
reports a typical case of this rare disorder which could well be a first report from
Nepal.
Keyword : Eosinophilic Fascitis, fibrosing disorders